Pulmonary alveolar proteinosis.
نویسندگان
چکیده
Pulmonary alveolar proteinosis is a rare cause of respiratory distress in neonates. We present a 4 month old infant who presented with progressive respiratory distress since birth and failure to thrive. He was initially treated as a case of diffuse alveolar disease but on open lung biopsy was diagnosed as pulmonary alveolar proteinosis. The child expired at 7 months of age.
منابع مشابه
Autoimmune pulmonary alveolar proteinosis co-existing with breast cancer: a case report
INTRODUCTION Pulmonary alveolar proteinosis is a rare pulmonary disease characterized by excessive alveolar accumulation of surfactant due to defective alveolar clearance by macrophages. There are only a few published case reports of pulmonary alveolar proteinosis occurring in association with solid cancers. To the best of our knowledge, there are no previously reported cases of pulmonary alveo...
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ورودعنوان ژورنال:
- Indian pediatrics
دوره 46 6 شماره
صفحات -
تاریخ انتشار 2009